Autoimmune Lymphoproliferative Syndrome Misdiagnosed as Hemophagocytic Lymphohistiocytosis A Case Report

Authors

  • E Shahverdi Students’ Research Committee (SRC), Baqiyatallah University of Medical Sciences, Tehran, IR Iran
  • F Dolatimehr Students’ Research Committee (SRC), Baqiyatallah University of Medical Sciences, Tehran, IR Iran
  • H Abolghasemi Department of Pediatrics , Baqiyatallah University of Medical Sciences, Tehran, IR Iran
  • R Mehdi Oghli Students’ Research Committee (SRC), Baqiyatallah University of Medical Sciences, Tehran, IR Iran
Abstract:

Autoimmune lymphoproliferative Syndrome (ALPS) is a rare inherited disorder of apoptosis. It usually presents with chronic lymphadenopathy, splenomegaly, and symptomatic cytopenia in a child. Herein, we report a 14-year-old boy with symptoms misdiagnosed as hemophagocytic lymphohistiocytosis who was treated before ALPS was diagnosed for the patient. This case should alert pediatricians to consider ALPS in differential diagnosis of a child with lymphadenopathy, splenomegaly, and cytopenia.

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Journal title

volume 7  issue None

pages  198- 200

publication date 2015-07

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